leg length discrepancy

aetiology
Interference with length

Decrease

Fracture

·      due to

·      angulation

·      overlap

Interference with growth

·      due to

·      genetic abnormality

·      damage to physis

·      alteration of forces

Inhibition

Congenital shortening

·      growth slowed

·      because of abnormal programming of genetic mechanism

Trauma

·      injury to physis

·      due to

·      direct injury to cells responsible for growth

·      formation of bony bridge

·      SH I and II fractures

·      occur through zone of hypertrophy (weakest)

·      do not involve area primarily responsible for growth

·      unlikely to interfere with growth

·      SH III and IV

·      cross growth zone

·      likely to result in growth arrest or bony bridge

·      SH V

·      involve whole physis

·      interfere with growth

Infection

·      may result in destruction of physeal cells

·      results in formation of large bony bridge

Paralysis

·      mechanism for growth inhibition unclear

·      may be due to

·      decreased blood flow from decreased muscle activity or abnormal vasomotor control

·      decreased compression across physis from reduced muscle activity

Tumour

·      due to

·      destruction of physis by tumour invasion

·      damage to physis by irradiation

·      origination of tumour from physis (enchondroma, osteochondroma)

Avascular necrosis

·      blood supply of physis from epiphyseal vessels

·      interference with epiphyseal blood supply also affects physis

Stimulation

·      probably due to increased circulation

Tumour

·      vascular malformations

·      haemangiomatosis

·      Klippel-Trenaunay-Weber

·      nonvascular tumours

·      neurofibromatosis

·      fibrous dysplasia

Inflammation

·      may be seen in

·      chronic osteomyelitis

·      juvenile rheumatoid arthritis

Fracture

·      of diaphysis

·      due to increased blood flow

·      most common in femoral shaft fractures

Summary

Congenital / developmental

·      terminal limb deficiencies

·      paraxial hemimelias

·      PFFD

·      hemiatrophy or hemihypertrophy

·      congenital pseudarthrosis of tibia

·      Ollier’s disease

·      CDH

Paralytic

·      polio

·      cerebral palsy

·      myelopathy

Infections

·      with growth retardation

·      with growth stimulation

Trauma

·      malunion

·      physeal damage

·      overgrowth

Tumours

·      overgrowth

·      fibrous dysplasia

·      osteoid osteoma

·      haemangioma

·      neurofibromatosis

·      retardation

·      enchondroma

·      bone cyst

·      neurofibromatosis

Apparent

·      pelvic obliquity

·      scoliosis

·      joint contracture

effect
Gait

Child

·      usually compensates well

·      walks on toes of short leg

·      results in smooth gait

·      only abnormality is lack of heel strike on short side

·      another possible compensation is flexion of knee of long leg

·      never done because too much effort required

Adult

·      compensates less well

·      walks with bilateral heel-toe gait

·      vaults over long leg

·      produces excessive up and and down motion of pelvis and trunk

·      results in increased energy expenditure

·      asymmetry of gait may persist with correction of leg length

·      knees at different levels

·      alters cadence of each leg

Hip

·      effect of two-legged stance is uncovering of hip of long leg

·      theoretical risk of development of degenerative arthritis

·      no evidence that this occurs

·      probably because little time spent in two-legged stance

Knee

·      one study showed increased knee pain in athletes

Spine

·      similar to hip

·      theoretical risk of developing scoliosis but no evidence

growth
Contribution

·      four physes contribute consistent proportions of growth

·      proximal femoral physis 1/8” / yr

·      distal femoral physis 3/8” / yr

·      proximal tibial physis 2/8” / yr

·      distal tibial physis 1/8” / yr

Relationships

·      relationship between

·      maturity (skeletal age)

·      stature (leg length)

·      aging (years of age)

Stature and age

·      steady growth occurs

·      growth spurt in early adolescence

·      cessation at 14-15 (girls) and 16-17 (boys)

Maturity and age

·      maturation can occur at different rates

·      if early, are tall early and stop growing early

·      can have spurt where mature more than age

·      pass through skeletal ages more quickly

Stature and maturity

·      reflected by Green and Anderson curves

·      growth vs skeletal age

·      shows no growth spurt

·      because growth spurt and maturation spurt occur together

assessment
History

·      determine cause

·      determine deformity

Examination

Leg length

·      apparent length

·      from umbilicus

·      real length

·      from ASIS

·      functional length

·      blocks

Other factors

·      pelvic obliquity

·      spine deformity

·      hip contractures

·      ankle contractures

·      knee deformities

·      joint stability

·      muscle power

Radiology

Leg length

Teleroentgenogram

·      single exposure of both legs

·      on long film with radiopaque ruler

·      advantages

·      single exposure

·      shows all of bones

·      disadvantages

·      inconvenient to handle

·      parallax errors

Orthoroentgengram

·      similar film

·      separate exposures of hip, knee and ankle

·      advantages

·      eliminates parallax error

·      disadvantages

·      multiple exposures (problem with movement)

Scanogram

·      similar separate exposures

·      film moved between exposures

·      advantages

·      smaller film

·      disadvantages

·      multiple exposures

CT scan

·      cuts taken through points of interest

·      distances between points measured

·      advantages

·      accurate

·      comparable cost

Skeletal age

·      comparison of x-rays with atlases

Greulich-Pyle atlas

·      x-rays of left hand and wrist

·      advantages

·      correlated with leg length (Green-Anderson)

·      disadvantages

·      large gaps in atlas

·      some children do not follow orderly progression

·      may be congenital anomalies of hand and wrist

Tanner-Whitehouse atlas

·      similar but more refined

·      20 specific landmarks graded

·      numerical score determined for each

·      skeletal age determined from total score

·      advantages

·      more accurate

·      disadvantages

·      more cumbersome and time consuming

·      not correlated with leg length

analysis
Arithmetic method

·      White/Menelaus method

·      rule-of-thumb method

·      less accurate

·      more convenient

·      based on following statements

·      girls stop growing at age 14

·      boys stop growing at age 16

·      distal femoral physis grows at 3/8” / yr (1 cm / yr)

·      proximal tibial physis grows at 2/8” / yr (0.6 cm/yr)

·      advantages

·      convenient

·      disadvantages

·      uses chronological age cf. skeletal age (error with variations in maturity)

·      uses approximation of growth curve (inaccurate in young children)

·      useful to determine if time to move to more accurate method

Technique

1.   determine past growth rate

·      growth rate of long leg (G) = past growth / time interval

2.   determine growth inhibition

·      inhibition (I) = (growth of long leg - growth of short leg) /                                                               growth of long leg

3.   determine future growth

·      future growth (FG) = G x yrs remaining

4.   determine future increase in discrepancy

·      future discrepancy (FD) = FG x I

5.   determine discrepancy

·      discrepancy = present discrepancy + FD

6.   predict effect of epiphseodesis

·      effect = growth rate x yrs remaining

Growth-remaining method

·      based on Green and Anderson tables

·      advantages

·      uses skeletal age

·      disadvantages

·      requires availability of and familiarity with graphs

Technique

1.   calculate growth inhibition as above

·      I = (growth LL - growth SL) / growth LL

2.   plot present length of long leg on leg-length vs age graph

3.   project to maturity to determine mature length of long leg

4.   calculate future growth of long leg

·      future growth (FG) = projected length - present length

5.   calculate future increase in discrepancy

·      future discrepancy (FD) = FG x I

6.   determine discrepancy as above

·      D = PD + FD

7.   predict effect of epiphseodesis

·      use growth-remaining vs age graph

Straight-line graph method

·      uses Green-Anderson data

·      based on principles

·      growth of legs can be represented graphically by straight lines

·      nomogram can be used to determine growth percentile from skeletal age and leg length

·      straight line produced by altering Green-Anderson tables

·      scale on X-axis manipulated

·      accuracy of data preserved

·      curve represented by irregularity of skeletal age lines

·      plotting length of leg on graph means

·      length of leg represented by vertical position

·      growth rate of leg represented by slope

·      discrepancy represented by vertical difference

·      inhibition represented by slope difference

Technique

1.   assess past growth

·      plot point for long leg on sloping line marked “LONG LEG”

·      draw vertical line through that point

·      plot point for short leg on that vertical line

·      plot point for skeletal age on vertical line

·      plot successive visits

·      draw straight line through short leg points

·      line represents growth of short leg

2.   assess future growth

·      draw horizontal line of best fit through skeletal age points

·      continue horizontal line to intersect line of maturity

·      draw vertical line from intersection point to growth lines of long and short leg

·      points of intersection indicate predicted lengths

3.   predict effect of surgery

·      draw lines parallel with reference lines

·      intersect these with vertical line of end of growth

·      points represent predicted lengths of long leg after different types of epiphyseodesis

Issues

Inhibition

·      methods use previous inhibition to predict future inhibition

·      assume that growth inhibition remains constant

·      usually true or not different enough to alter validity of prediction

Inadequacy of data

·      three possibilities

1.   continuing inhibition but time of onset known

·      can use straight line graph and assume equal leg lengths at time of onset

2.   static discrepancy

·      eg. stimulation from previous osteomyelitis or fracture, discrepancy from fracture malunion

·      can assume discrepancy at maturity will be same as now

3.   no assumptions reasonable

·      reassess at maturity

treatment
Goals

Equal leg length

·      goal with mild to moderate isolated discrepancy

Unequal leg length

·      goal with paralysis

·      should be 1-2 cm shorter to allow clearance

Level pelvis

·      goal with deficiencies in pelvis

·      should use blocks to estimate functional correction

Vertical lumbar spine

·      goal with pelvic obliquity

·      vertical spine more important than level pelvis

Equalisation with prosthesis

·      goal with excessive discrepancy

·      traditionally described as

·      femur less than half length of other side

·      discrepancy > 15 cm

·      may require

·      knee fusion

·      Syme amputation

·      van Ness rotationplasty

Coexistent problems

·      may require correction of other problems that are prerequisites

·      release of contractures

·      correction of angular deformity

·      correction of spinal deformity

·      excision of bony bridge

·      completion of partial arrest

Principles

1.   correct coexisting deformities first

·      deformity may adversely affect outcome

·      correction may partly address discrepancy

2.   choose treatment according to projected discrepancy

·      0-2 cm - no treatment

·      2-6 cm - shoe lift, epiphyseodesis

·      6-15 cm - lengthening

·      > 15 cm - prosthesis

Nonoperative

Shoe lift

·      excellent treatment for discrepancy 2-5 cm

·      < 2 cm - not required

·      > 5 cm - recurrent ankle sprains

·      aim is to improve gait

Prosthetic fitting

·      last resort

·      often combined with amputation

·      useful for

·      large discrepancies

·      deformed and functionally useless feet

·      best for discrepancies

·      > 15 cm

·      > 1/2 femur

·      advantages

·      one hospitalisation

·      good functional outcome

·      optimal time

·      Symes - age 1

·      van Ness - age 3

Operative

Epiphyseodesis

·      often treatment of choice

Advantages

·      low morbidity

·      usually accurate

·      easy to perform

Disadvantages

·      operation on normal leg

·      loss of height

Indications

·      anticipated discrepancy of 2-6 cm

·      less well tolerated for > 6 cm discrepancy

·      significant loss of height

·      disproportionate appearance

Principles

·      involves inducing known amount of growth inhibition

·      3/8” / yr or 38% for distal femoral physis

·      2/8” / yr or 27% for proximal tibial physis

·      5/8” / yr or 65% for both

·      desired shortening achieved by operating at exactly the right time

·      may choose to wait and perform femoral and tibial epiphyseodesis later

·      thus may be able to achieve knee joints being at same level

·      aim to produces 0.5-1 cm undercorrection

·      operate a little later than calculated

·      better to undershorten rather than overshorten

Technique

·      creation of symmetric bony bridge

·      medial and lateral approaches

·      physis identified

·      window  removed to gain acess to physis

·      circular or rectangular

·      plate excised in entire thickness

·      with curette

·      window reorientated to act as bone graft

·      circular rotated through 90o

·      rectangular rotated through 180o

·      fusion occurs within 8 wks

Complications

·      failure of complete closure

·      continued growth

·      angular deformity

Femoral shortening

·      similar indications to epiphyseodesis

·      used in patients

·      who are too old

·      in whom confident prediction of discrepancy at maturity cannot be made

·      diaphyseal shortening of maximum of 5 cm

·      fixed with IM nail

·      complications

·      disadvantages quadriceps

·      rotatory malalignment

·      malunion or nonunion

·      infection

Growth stimulation

·      concept of stimulation of physis as occurs in fracture

·      many methods tried

·      none successful enough to be clinically useful

Leg lengthening

·      uses concept of distraction osteogenesis

·      osteotomy

·      pins proximal and distal to osteotomy

·      controlled distraction

·      formation of bone in zone of distraction

Advantages

·      maintains height and proportions

·      avoids operation on normal side

Disadvantages

·      difficult and protracted

·      high rate of complications

Preoperative assessment

·      patient psyche and social situation

·      able to cope with psychological implications

·      location of discrepancy

·      general medical problems

·      local orthopaedic problems

·      status of adjacent joints

Indications

·      discrepancy 6-15 cm

·      < 6 cm - epiphyseodesis or shortening technically easy, low morbidity and acceptable result

·      > 15 cm - risks outweigh benefits

Contraindications

·      sensory or motor deficits

·      significantly deformed or dislocated joints that cannot be stabilised

·      psychological problems

Technique

·      osteotomy performed

·      drill-holes and closed osteoclasis in attempt to preserve periosteum

·      device applied

·      uniplanar device (Wagner, Orthofix)

·      circumferential device (Ilizarov)

·      distraction commenced

·      for tibial lengthening, should first perform

·      heel cord lengthening

·      screw fixation of distal part of fibula

·      halt or slow lengthening with

·      insufficient new bone formation

·      nerve parasthesias or palsies

·      compartment syndrome

·      equinus deformity

·      joint loss of motion or subluxation

·      psychological reactions

·      adjust fixation with

·      development of angular deformity

·      once desired lengthening achieved, options are

·      maintenance of external fixation device

·      insertion of plate +/- bone graft

·      protective brace

Concepts

·      minimal disturbance of bone

·      preserves intramedullary contents and blood supply

·      metaphyseal lengthening

·      more active osteoblasts

·      greater cross-sectional area and thus strength

·      two-level lengthening

·      for significant discrepancy

·      delay before distraction

·      of 10 days

·      to allow establishment of osteogenic process

·      slow rate of distraction

·      optimum is 1 mm/day

·      rhythm of distraction

·      optiumum is 4 times a day

Problems

·      limitations due to biological capabilities of

·      muscles

·      ligaments

·      neurovascular structures

·      adjacent joints

·      problems due to

·      overstretching

·      insufficient fixation

·      interference with blood supply

·      nontechnical problems related to

·      physical and emotional stability of patient and family

·      doctor-patient relationship

Complications

·      of pins

·      neurovascular injury

·      pin tract infection

·      failure

·      mechanical failure of device

·      fracture of bone

·      joint subluxation

·      knee

·      hip

·      delayed union

Distraction epiphyseolysis

·      tibial lengthening by distraction across proximal physis

·      similar amount of lengthening and complications to conventional lengthening

·      continuing research