Post-traumatic osteonecrosis

intracapsular femoral fracture
Radiology

Plain x-ray

·      usually first recognised when there is structural failure and collapse of joint surface

·      has been recognised as early as 6 months

·      in most patients does not appear for more than 1 year

·      may be delayed up to 2.5 years

·      if patient immobilised, may see relative increase in density of dead bone

·      less common with internal fixation and early mobilisation

Bone scan

·      earliest indication given by bone scan

·      ‘cold’ femoral head

·      prognostic value limited

Blood supply

·      if fracture displaced, inevitable that superior retinacular vessels damaged

·      potential for recovery depends on

·      inferior retinacular vessels

·      artery from ligamentum teres

·      if fracture displaced, ischaemia can still occur

·      from traumatic haemarthrosis

·      causes raised intra-articular pressure and venous obstruction

Incidence

Necrosis

·      1/3 of heads completely viable

·      1/3 of heads have some viable bone

·      almost always as wedge based on fovea

·      may be only a few mm in depth

·      may be all of head inferior to upper fovea

·      necrosis most common in anterosuperolateral subchondral region

·      1/3 of heads have little or no viable bone

Revascularisation

·      rapid if large viable wedge in fovea

·      slow if completely necrotic

·      relies on growth of vessels across fracture

·      growth across fracture may be impeded by

·      movement at fracture

·      continuing impaction of head

·      organisation and fibrosis of soft tisse and clot across fracture

·      last area to regain supply is superolateral subchondral region

Fracture healing

·      75% of fractures unite

·      union dependent on

·      mechanical factors (stability)

·      vascular factors (viability)

·      union more likely with viable or at least partly viable head

Late collapse

·      occurs in 20% of fractures

·      more common

·      in displaced fractures

·      in fractures in extreme valgus

·      where all or most of femoral head necrotic

·      unclear whether influenced by

·      type of fixation device

·      delay to reduction

·      once collapse occurs

·      osteophytes develop at living margin of femoral head

·      joint space diminishes when articular sequestrum disintegrates

·      disability varies

·      20% symptom-free

·      50% mild-moderate disability

·      30% severe disability

hip dislocation

·      incidence of femoral head necrosis is 15%

·      increased incidence with

·      associated acetabular lip fracture

·      following open reduction

·      when reduction delayed > 24 hrs

·      ischaemia from damage to retinacular vessels

·      rupture of capsule at base of neck

·      constriction of capsule if femoral head buttonholes through it

fracture of talus

·      incidence of necrosis increases with displacement

·      Hawkins 1 - rare

·      Hawkins 3 - 35%

·      union usually occurs

·      subtalar arthritis common

fracture of scaphoid

·      occurs in 10-15% of fractures

·      more common with

·      displaced fractures

·      fractures with carpal dislocations

·      usually affects proximal pole

·      if revascularisation incomplete

·      proximal pole collapses

·      degenerative arthritis occurs

Dysbaric osteonecrosis

types
Compressed air workers

Conditions

·      compressed air used in construction of tunnels under rivers or harbours to preven water seeping through ground

·      pressures required usually 4 atm

·      workmen compressed and decompressed in manlocks

·      time for decompression depends on working pressure and time

Incidence

·      incidence is 20%

·      50% have more than one lesion

·      2/3 are clinically silent shaft marrow infarcts

·      1/3 are juxta-articular lesions

·      1/3 of these produce symptoms from structural failure and collapse

·      most common sites are

·      distal femoral shaft (40%)

·      proximal tibial shaft (20%)

·      humeral head (25%)

·      femoral head (10%)

Divers

Conditions

·      professional divers at greater risk

·      work from dive bell or connected to surface by lines

·      exposed to prolonged high pressures

·      recreational divers

·      have limited exposure time because of SCUBA gear

·      are exposed to limited depths

Incidence

·      varies according to stringency of decompression

·      50% in Japanese shellfish divers

·      5% in British Navy

·      80% are marrow infarcts

·      20% are juxta-articular

·      only 15% progress to structural failure

·      most common sites are

·      distal femoral shaft (60%)

·      proximal tibial shaft (20%)

·      humeral head (20%)

·      femoral head (1%)

factors
Pressure

·      unlikely to occur

·      compressed air pressure < 1.2 atm

·      diving depth < 30 m

Decompression sickness

·      incidence higher in those who have suffered decompression sickness

Number of exposures

·      increasing numbers of exposures increase the risk

aetiology and pathogenesis
Decompression

·      during compression, increased pressure causes nitrogen to become dissolved in tissues

·      during decompression, dissolved nitrogen cleared by circulation

·      removed in expired air by pressure gradient in alveoli

·      showers of nitrogen bubbles can occur in circulation and tissues

·      may be silent wrt. decompression sickness but may lead to bone necrosis

·      bone more prone to necrosis

·      fatty marrow remains supersaturated following decompression

·      intravascular and extravascular gas bubbles can occur

·      have intravascular occlusive effect and extravascular compressive effect

·      tissue disruption may cause fat emboli

·      result is ischaemia

Lesions
Medullary

·      most common in distal femur

Clinical

·      asymptomatic

Radiological

·      small dense areas with irregular outlines in medulla

·      may progress to linear streaks

Juxta-articular

·      most common in humeral head

Clinical

·      usually sudden onset of shoulder pain

·      ROM usually not severely limited

Radiological

·      small dense areas with irregular outlines adjacent to joint

·      may coalesce to give snow-cap appearance

·      dense linear opacity may traverse bone

·      dysbaric form characterised by

·      multiple small lesions due to small vessel occlusion

·      dense appearance due to calcification

·      collapse not inevitable, even with large necrotic areas

·      if occurs, changes then as in general form

·      osteophyte formation

·      degenerative osteoarthritis

Management
Medullary lesions

·      allowed to continue

·      no evidence that have increased risk of juxta-articular lesions

Juxta-articular lesions

·      advised to stop work

arthroplasty usually not indicated because patients are young manual workers

Gaucher’s disease

epidemiology and aetiology

·      develops in children and adolescents

·      most common in Ashkenazi (European) Jews

·      autosomal recessive

·      due to deficiency of lysosomal enzyme glucocerebroside hydrolase

·      results in accumulation of insoluble glucosylceramide in cells of monocyte-macrophage system

·      type 1 (90%) associated with orthopaedic problems

Pathogenesis

·      most likely due to packing of marrow spaces with bloated macrophages

·      leads to

·      compression of intraosseous sinusoids

·      scarring and further ischaemia

clinical

·      results from accumulation of large macrophages rich in glucosylceramide in

·      liver

·      spleen

·      bone marrow

·      produces (with increasing severity)

·      focal radiolucent areas in long bones

·      cortical thinning and flask-shaped metaphyses (Erlenmeyer flask)

·      pathological fracture

Medullary

·      most medullary infarcts are asymptomatic

·      may develop acute ‘bone crisis’

·      like sickle cell disease

·      difficult to differentiate from osteomyelitis

·      pain settles after few days

·      then develop large medullary infarction on x-ray

Juxta-articular

·      most commonly involves femoral heads

·      in children, similar to Perthes’ disease

·      in adults, similar to idiopathic necrosis

treatment

·      new development is enzyme replacement

Sickle cell disease

epidemiology and aetiology

·      seen in Africans incl. Negroes

pathogenesis
Haemoglobin

·      Hb is tetramer

·      two pairs of polypeptide chains (alpha, beta, gamma or delta)

·      adult Hb is

·      97% HbA (alpha2, beta2)

·      3% HbA2 (alpha2, delta2) (increased in thalassaemia)

·      foetal Hb is HbF (alpha2, gamma2)

Sickle cell

·      abnormality is peptide substitution in beta chain

·      abnormal haemoglobin designated HbS cf. HbA

Sickle cell disease

·      two abnormal genes related to haemoglobin formation

·      homozygous sickle cell disease (Hb SS)

·      combination of HbS with another haemoglobinopathy  (Hb SC)

·      combination of HbS with thalassaemia (Hb SThal)

·      sickling occurs in sickle cell disease with relative hypoxia

Sickle cell trait

·      sickle cell gene with normal adult haemoglobin gene

·      heteroxygous Hb SA

·      sickling only occurs in sickle cell trait with extreme hypoxia

·      under anaesthesia, in extreme cold, at high altitudes

·      patients have slight protection against falciparum malaria

Sickling

·      HbS changes shape when deoxygenated

·      red cell assumes sickle shape

·      may become trapped in capillaries

·      leads to vascular occlusion,  infarction and thrombosis

clinical

·      two main problems

1.   vaso-occlusion

·      suffer recurrent crises of  abdominal and bone pain

2.   anaemia

·      sickled cells have shorter lifespan

Bone crises

·      due to bone infarcts

·      acute episodes of pain and tenderness

·      may be fever and leukocytosis

·      may affect several bones

·      if end of long bone affected, develop joint pain and effusion

Diaphyseal necrosis

·      usually involves shaft near metaphysis of

·      femur

·      tibia

·      humerus

·      endosteal vessels occluded

·      periosteal vessels remain viable

Young children

·      usually associated with bone crisis

·      x-ray changes usually resolve

Older children and adults

·      often clinically silent

·      x-ray changes do not resolve

·      may be sclerotic areas from

·      calcification

·      new bone formation

·      extensive subperiosteal reaction may give appearance of bone in bone

Juxta-articular necrosis

·      most common site is osteonecrosis of femoral head

Children

·      occurs in 10% (50% asymptomatic)

·      similar picture to Perthes’ disease

·      may involve part or all of epiphysis

Adults

·      occurs in 40%

·      similar pattern to idiopathic necrosis

Hand-foot syndrome (dactylitis)

·      seen in children age 6-24 mths

·      appears as HbF disappears and HbS appears

·      dorsum of hands and feet become swollen and painful

·      symptoms subside after 1-2 wks

·      x-ray changes at 2 wks

·      reflect absence of endosteal blood supply and presence of periosteal blood supply

·      subperiosteal new bone formation

·      patchy erosion of cortex by periosteal granulation tissue

·      bone may remodel and return to normal

·      growth may cease temporarily

Osteomyelitis

·      bone crises diffficult to distinguish from osteomyelitis

·      bone marrow infarct may become secondarily infected

·      increased risk of infection because of impairment of splenic function

·      Salmonella often involved from ischaemic bowel

Radiation osteonecrosis

epidemiology

·      seen with high-dose therapy

·      due to

·      direct cellular damage

·      vascular narrowing

·      most common in women

·      pelvis and upper femur for gynaecological tumour

·      shoulder for breast cancer

pathology

·      bone formation rather than resorption inhibited

Cortex

·      small cortical defects filled with fibrous tissue

·      due to failure of filling in of resorption areas

Medulla

·      marrow spaces filled with fibrous tissue

·      often patchy calcification

Proximal femur

·      typical osteonecrosis may occur

·      pathological fracture may occur

·      ‘stress fracture’ with slow slip into varus

·      due to osteoporosis rather than osteonecrosis

X-ray

·       result is irregular patches of increased and decreased radiodensity

·      should not be assumed to be metastases from original cancer

Osteonecrosis of the knee

spontaneous
Clinical

·      usually healthy woman age 60+ yrs

·      sudden onset of severe knee pain

·      almost always medial femoral condyle

·      exquisite local tenderness

·      may be effusion

·      other side rarely involved

Pathology

·      initially localised depression of condylar surface

·      then articular sequestrum becomes partially separated as hinged flap

·      may separate completely

·      result is crater with base of fibrocartilage

Radiology

X-ray

·      initially normal

·      later develop

·      subchondral lucent line (crescent sign)

·      flattening of condyle

·      patchy sclerosis

·      may be rapid collapse with varus deformity

Bone scan

·      focal increase in uptake

MRI

·      discrete well-defined low-signal areas in subchondral region

Secondary

·      secondary to

·      steroid therapy

·      SLE

·      sickle cell disease

·      much less common

Clinical

·      gradual onset of pain

·      lateral condyle in 60%

·      bilateral in 50%

·