avascular necrosis

General

Definition

·      in situ death of a segment of bone due to ischaemia

·      multifactorial heterogenous group of disorders that lead to common final pathway of bone death

location

·      femoral head

·      humeral head

·      scaphoid

·      lunate

·      talus

·      femoral condyles

·      capitellum

aetiology

Traumatic

·      fractures

·      dislocations

Nontraumatic

·      corticosteroid use

·      alcohol abuse

·      sickle cell disease

·      dysbarism

·      Gaucher’s disease

·      radiation

Pathogenesis

·      due to ischaemia of bone

·      numerous theories

·      are mutual rather than exclusive

Interruption of arterial supply

·      fracture

·      dislocation

·      slipped upper femoral epiphysis

·      post-treatment of CDH

Capillary occlusion by embolism or thrombus

·      dysbarism (nitrogen bubbles)

·      corticosteroids (fat emboli)

·      alcohol (fat emboli)

·      sickle cell disease (abnormal red cells)

Injury to vessel wall

·      radiation injury

·      vasculitis (SLE)

Intraosseous capillary tamponade

·      Gaucher’s disease (bloated macrophages)

·      corticosteroids (enlarged marrow fat cells)

·      alcohol (enlarged marrow fat cells)

·      post-infection (inflammatory response)

Pathology
Stages

Death

·      some ischaemic event occurs

·      segment of bone dies

·      marrow cells die within 6-12 hrs

·      osteocytes die within 12-48 hrs

Revascularisation

·      capillaries and mesenchymal cells grow in from abutting live marrow

·      grow into dead marrow spaces

·      mesenchymal cells differentiate

Repair

·      macrophages remove dead fat and cellular debris

·      dead bone resorbed by osteoclasts

·      new bone laid down on surface of dead trabeculae by osteoblasts

·      if healing incomplete, dead bone replaced by fibrous tissue and granulation tissue

Juxta-articular necrosis

·      most commonly affects

·      anterosuperolateral portion of femoral head

·      central dome of humeral head

·      femoral condyles

·      talus

·      scaphoid

·      lunate

·      capitellum

Stage 1 - before onset of structural failure and collapse

·      patient symptom-free

·      joint contour normal

Pathology

·      articular cartilage normal

·      beneath articular cartilage is variable depth of

·      opaque yellow marrow

·      bone trabeculae devoid of osteocytes

·      dead tissue separated from underlying living bone by

·      dense fibrous layer

·      vascular granulation tissue

·      in border zone,  trabeculae broadened by formation of new bone on surface

Radiology

·      death of bone does not alter its radiological density

·      if area immobilised

·      living bone becomes porotic due to osteoclastic bone resorption

·      dead bone appears relatively denser

·      after a period

·      cystic areas appear within lesion due to osteoclastic resorption

·      irregular mottled areas of increased density appear at junction of living and dead bone due to new trabecular bone

·      coalesce to form compact sclerotic line

Stage 2 - structural failure and collapse

·      marked by sudden onset of pain

Pathology

·      due to incomplete healing response

·      occurs in 90%

·      resorption > formation

·      trabecular microfractures occur in dead bone

·      leads to weakening and fracture

1.   subchondral fracture

·      immediately below subchondral plate

·      produces thin articular sequestrum (eggshell)

·      joint contour initially appears normal

·      wrinkle then appears at dead margin

·      then cracks and fissures appear

·      escape of bony detritus through crack into joint leads to synovitis

·      fibrocartilage may form on undersurface of sequestrum

·      sequestrum may become reattached by fibrocartilage

·      sequestrum may be ground away

·      fibrocartilage may be exposed to form new joint surface

2.   deep fracture

·      trabecular fracture may occur more deeply

·      at junction between living and dead bone

·      large sequestrum sinks into femoral head

·      uncollapsed margin may produce ring-like ridge

Radiology

·      area of dead bone may appear dense due to

·      compression of dead trabeculae

·      calcification of dead marrow or debris

1.   subchondral fracture

·      trabecular fracture appears as lucent crescentic line running parallel to joint surface

·      ‘crescent sign’

·      in hip, best seen on frog-leg lateral

2.   deep fracture

·      no crescent sign

·      articular step seen beneath acetabular margin and at fovea

Stage 3 - development of secondary arthritis

Pathology

·      joint incongruity leads to loss of articular cartilage

·      osteophytes form

Medullary necrosis

·      asymptomatic

·      occurs with

·      dysbarism

·      haemoglobinopathies

·      Gaucher’s disease (occas.)

·      most commonly affects

·      lower femoral shaft

·      upper tibial shaft

·      upper humeral shaft

·      extent varies

·      small foci

·      large areas involving endosteal cortex

Pathology

·      dead marrow is yellow and opaque

·      surrounded by dense collagen layer

·      collagen may be calcified

·      bone trabeculae at margin may be broadened by repair

·      if endosteal cortex involved, cortical width increased

Radiology

·      main change is calcification

·      if occurs in collagen layer, is wavy line of increased density

·      ‘coil of smoke’ sign

·      endosteal cortex may be thickened

·      may be difficult to distinguish from

·      calcified enchondroma

·      bone island

Investigation
Plain films

·      early changes

·      mottling

·      sclerotic line at junction between dead and living bone

·      late changes

·      crescent sign

·      segmental collapse

·      end-stage changes

·      osteoarthritis

·      until osteoarthritis develops, joint space maintained

Bone scan

·      initially absent or decreased uptake seen due to avascularity

·      does not absolutely predict necrosis as revascularisation may occur

·      later increased uptake seen due to repair

·      does not absolutely predict good outcome as revascularisation may not be adequate or permanent

·      non-specific

·      cold areas may be due to metastatic deposits

·      hot areas may be due to any cause of increased bone vascularity or formation

·      most useful to detect avascularity following acute femoral neck fracture or hip dislocation

CT scan

·      not useful early

·      can be used in later stages to assess

·      extent of subchondral fracture

·      flattening and collapse of articular surface

MRI

·      most sensitive and specific method

·      proximal femur most extensively studied

Changes

Normal

·      on T1 image

·      normal medullary cavity emits strong signal (white) from hydrogen-rich fatty marrow

·      normal cortex and subchondral plate emit weak signal (black)

Necrosis

·      T1 shows low-signal line

·      corresponds to sclerotic line on x-ray

·      takes weeks to develop

·      area cupped by low-signal band shows varying amount of decreased signal signifying dead bone

·      T2 shows characeristic double line

·      outer low-signal line related to thickened trabeculae

·      inner high-signal line related to granulation tissue

Advantages

·      able to identify necrosis in high-risk patients in pre-radiological state

·      accurately reveals site and extent of bone death

Functional exploration

·      three-phase invasive investigation developed by Ficat

·      no longer routinely used if MRI available

Intraosseous pressure

·      intertrochanteric cannula inserted

·      bone marrow pressure measured

·      abnormal if

·      baseline pressure > 30 mm Hg

·      pressure > 30 mm Hg 5 min after injection of 5 ml isotonic saline

·      oxygen saturation of blood from cannula > 85%

Intramedullary venogram

·      10 ml contrast injection

·      abnormal if

·      injection difficult and painful

·      diaphyseal stasis or reflux seen at 15 min

Biopsy

·      trephine from greater trochanter to within 5 mm of articular cartilage

·      abnormal if

·      marrow necrosis

·      medullary and trabecular necrosis

·      necrosis with marrow fibrosis and appositional new bone